Tumors located in the distal extremities such as the hands or feet may only present clinically with signs of painless swelling 5. Treatment for cmf requires surgery to remove the tumor. To present a case of chondromyxoid fibroma of the nasal bone and discuss its presentation. Chondromyxoid fibroma cmf is one of the rarest of bone tumors, accounting for less than 1% of all bone tumors. Chondromyxoid fibroma of the rib initially seen as a. Chondromyxoid fibroma is a benign, although potentially aggressive tumor, with a cartilagelike matrix, accounting for approximately 1% of all bone tumors. Summary of the site and distribution of chondromyxoid fibromas in our. Rarer locations include the fibula, scapula, vertebrae and ribs 3. Wed like to understand how you use our websites in order to improve them. Bullous lesions in patient with lupus explore this issuefebruary 2016 her chest radiograph revealed no infiltrates. The presence of this tumor was heralded solely by aural fullness caused by otitis media with effusion.
Open access publication chondromyxoid fibroma of the foot. A rare case of juxtacortic chondromyxoid fibroma in. Pdf chondromyxoid fibroma cmf is one of the rarest benign tumors of cartilaginous origin. The tumor with a thin scalloped, sclerotic border has an eccentric location in the metaphysis and a translucent, osteolytic, bubbly appearance. Calcification was seen in more than one third of the cases but was rarely. A rare case of chondromyxoid fibroma mimicking spina ventosa. We describe a case of chondromyxoid fibroma of the mastoid bone extending along the occipital bone in a 48yearold man. Chondromyxoid fibroma is an uncommon benign cartilaginous tumor accounting for less than 1% of all bone tumors. In 1948, the tumor was first described by jaffe and lichtenstein as a lesion derived from cartilageforming tissue and composed of various proportions of chondroid, fibrous, and myxoid tissues. We report a case of a 35yearold female with a 3 month history of lower back pain after sustaining a fall on her sacrumcoccyx presenting with a progressive complaint of localized lower back pain, occasional urinary retention without incontinence, gluteal hypesthesia, and. Males have a higher incidence, with no other demographic bias 3. Chondromyxoid fibroma cmf is a relatively uncommon benign bone.
This article is from archives of plastic surgery, volume 41. Soni r, kapoor c, shah m, turakhiya j, golwala p 2016 chondromyxoid fibroma. Radiographic and histologic patterns of calcification in chondromyxoid fibroma. Benign cartilaginous tumor made of lobulated, fibromyxoid, and chondroid tissues. Only 2 of the 50 cmf included in their study occurred in the skull. Dahlin dc 1956 chondromyxoid fibroma of bone, with amphasis on its morphological relationship to benign chondroblastoma. Chondromyxoid fibroma cmf is perhaps the rarest of all. The classic site of involvement is the metaphyseal region of long tubular bones.
The most commonly affected area is the metaphysial region of the proximal tibia and the distal femur 2. Chondromyxoid fibroma of the distal fibula in a pediatric patient. Chondromyxoid fibroma cmf is one of the rarest benign tumors of cartilaginous origin. Huge chondromyxoid fibroma of the right iliac wing with tremendous soft tissue extensions hosameldeen mostafa ali, md department of radiology, benha university, benha, egypt address correspondence to.
Chondromyxoid fibroma cmf is a benign cartilaginous neoplasm first distinguished from other cartilaginous tumors by jaffe and lichenstein in 1948. Pdf chondromyxoid fibroma of the finger researchgate. Chondromyxoid fibroma cmf is an extremely rare, benign cartilaginous tumor that makes up case description. The following is the supplementary data to this article. July 27, 2017 056 the tumor may be discovered incidentally during radiography 1. It is a benign noncancerous tumor that most often develops in older children and young adults under 30 years of age. Cmf is most often found in the long tubular bones, especially the tibia and femur near the knee joint. Wu ct, inwards cy, olaughlin s, rock mg, beabout jw, unni kk.
Mr images of 19 histopathologically confirmed chondromyxoid fibromas were retrospectively analyzed for signal. Many programs, including microsoft word, have the ability to open and edit pdf files. Chondromyxoid fibroma is a very rare benign cartilaginous tumor representing less than 0. Tinu syndrome with concomitant synovitis rheumatology case report. Chondromyxoid fibromas cmfs are extremely rare, benign cartilaginous neoplasms that account for chondromyxoid fibroma. We present the case of a 62yearold woman with chondromyxoid fibroma of the sphenoid sinus. The tumor cells were spindleshaped or stellate and arranged in a myxoid matrix. Concomitant lupus with features of scleroderma, castleman disease rheumatology case report. Article information, pdf download for chondromyxoid fibroma of the.
Chondromyxoid fibroma cmf is a benign, locally aggressive tumor of cartilaginous origin and accounts for less than 0. Radiological evaluation of a chondromyxoid fibroma published. Both clinically and histologically, it is a difficult diagnosis and can be confused with malignant lesions. Pdf on may 1, 2014, somin hwang and others published chondromyxoid fibroma of the. Complete local excision with tumorfree margins avoids the recurrence of cmf, the underlying tumor in this case report. Wenzel departments of radiology and oral and maxillofacial surgery, royal dental college, aarhus, denmark received 4 june 1990 and in final form 10 august 1990 a case of recurrence of a chondromyxoid fibroma 3 years after its surgical removal is presented. Chondromyxoid fibroma of the maxillofacial region is typically seen in patients. It is composed of a mixture of chondroid, myxoid, and fibrous tissues. Chondromyxoid fibroma is a rare benign tumor that usually occurs in the long bones and rarely affects the sinonasal region. Chondromyxoid fibroma with secondary aneurysmal bone. Chondromyxoid fibroma cmf is a rare, benign tumor of the bone that was described by jaffe and lichenstein in 1948. Chondromyxoid fibroma, which is a relatively late addition to the family of bone tumors, is a rare lesion that occurs in less than 1% of bone tumors and tumorlike lesions. Chondromyxoid fibroma cmf is a rare, benign bone tumour. The diagnosis of cmf depends upon its characteristic histological appearance like a lobular pattern with stellateshaped cells in a myxoid or.
To describe the mr findings of chondromyxoid fibroma. For establishing the diagnosis of chondromyxoid fibroma, histopathological examinations are essential. Desmoplastic fibroma df is a rare, benign but locally aggressive, intraosseous lesion with a high tendency of local recurrence. Only 2 of the 50 chondromyxoid fibromas included in their study occurred in the skull. Chondromyxoid fibroma is a benign tumor of bone that is characterized by chondroid and myxoid differentiation and by ultrastructural and immunohistochemical evidence of chondral origin. Huge chondromyxoid fibroma of the right iliac wing with. Furthermore, it shows a slightly expansile growth to the adjacent soft tissue. Brachyury staining was further performed in the following 2 categories. Primary chondromyxoid fibroma of the sternum is quite rare, with only six cases documented in the literature see table 1. The treatment of the secondary abc is based on the appropriate treatment for the underlying tumor. Moreover, a report of an interesting case is included localized in the mandibular corpus. It is associated with high local recurrence rates with a small risk file as a pdf without needing additional software or addins. To our knowledge, this is the first reportable case of cmp presenting with undifferentiated connective tissue.
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